Anesthetic Management of a Boy with Congenital Disorder of Glycosylation CDG I-xReport as inadecuate




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Congenital disorders of glycosylation CDGs are group group of genetic defects in the assembly and processing pathway of protein glycosylation, which cause a wide range of multi system dysfunction. This paper describes the anesthetic management of 6 year old boy with CDG type I-x for upper airway surgery. We used a sevoflurane-nitrous oxide-remifentanil regime with no complications and good results. As for now, the literature lacks reports of anesthetic management of children with CDG I-x, and this report may provide clinicians an option for safe anesthetic management.

KEYWORDS

Anesthesia, Pediatric, Metabolic Disorders, Congenital Disorders of Glycosylation, CDG

Cite this paper

A. Lehavi, H. Mandel and Y. Katz -Anesthetic Management of a Boy with Congenital Disorder of Glycosylation CDG I-x,- International Journal of Clinical Medicine, Vol. 2 No. 3, 2011, pp. 325-327. doi: 10.4236-ijcm.2011.23056.





Author: Amit Lehavi, Hanna Mandel, Yeshayahu Shai Katz

Source: http://www.scirp.org/



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