Papillon-Lefèvre syndrome and squamous cell carcinoma: a case reportReport as inadecuate

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Cases Journal

, 2:7067

First Online: 28 August 2009Received: 14 April 2009Accepted: 12 August 2009DOI: 10.4076-1757-1626-2-7067

Cite this article as: Al-Benna, S., Hasler, R., Stricker, I. et al. Cases Journal 2009 2: 7067. doi:10.4076-1757-1626-2-7067


Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory.

AbbreviationsPLSPapillon-Lefèvre syndrome

SCCsquamous cell carcinoma.

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Author: Sammy Al-Benna - Raphael Hasler - Ingo Stricker - Hans-Ulrich Steinau - Lars Steinstraesser


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